Author Archives: chang xu

Annotated Bibliography

 Almén, M. S., Jacobsson, J. A., Moschonis, G., Benedict, C., Chrousos, G. P., Fredriksson, R., & Schiöth, H. B. (2012). Genome wide analysis reveals association of a FTO gene variant with epigenetic changes. Genomics, 99(3), 132-137.

A genome wide DNA methylation profile was used to determine which genes were differentially methylated in carriers of the FTO risk allele (rs9939609). They identified 20 different sites associated with obesity. Overall this paper wasn’t extremely helpful for my project but allowed me to understand the characteristics of the FTO gene and how the risk allele can be mediated by epigenetic changes.

 

 Church, C., Moir, L., McMurray, F., Girard, C., Banks, G. T., Teboul, L., … Cox, R. D. (2010). Overexpression of Fto leads to increased food intake and results in obesity. Nature Genetics, 42(12), 1086–1092.

This study shows how overexpression of the FTO gene leads to increases in body and fat mass regardless of whether they were fed a normal or high fat diet. The increased body mass as primarily the result of increased food intake. This paper was useful in that it sparked my interest in how FTO overexpression resulted in increased obesity risk. They also looked at the effects diet had on the resulting phenotype, which I also based my experiment on.

 

Hess, M. E., Hess, S., Meyer, K. D., Verhagen, L. A., Koch, L., Brönneke, H. S., … & Belgardt, B. F. (2013). The fat mass and obesity associated gene (Fto) regulates activity of the dopaminergic midbrain circuitry. Nature neuroscience, 16(8), 1042-1048.

This paper showed how inactivation of the FTO gene resulted impaired dopamine receptor functions governing the neuronal DA signaling pathway. They compared the genes Drd3, Kcnj6, and Grin1 which are all key regulators of the DA pathway. Results showed that mRNAs had increased m6A methylation and protein expression was attenuated. This paper was extremely important to my experiment as it introduced me to the genes specific to the DA pathway which were affected by epigenetic modifications when FTO expression changed. It also provided me a basis for my experimental design and I ended up basing my methods on the MeRIP-Seq technique they used.

 

Ishii D, Matsuzawa D, Matsuda S, Tomizawa H, Sutoh C, Shimizu E (2014) Methyl Donor-Deficient Diet during Development Can Affect Fear and Anxiety in Adulthood in C57BL/6J Mice. PLoS ONE 9(8): e105750.

Methyl donors, such as folic acid, methionine, and choline are related to one-carbon metabolism and mediate methylation. This study examines the effects of methyl donor deficiency during a developmental period in fear memory acquisition/extinction and anxiety-like behavior. Results showed that methyl donor deficiency caused mice to have an impaired fear memory acquisition and reduced anxiety-like behavior by decreasing the expression of Dnmt3a, Dnmt3b, Grin2b and Gabar2. This paper mainly introduced me to the idea of methyl donor supplementation and helped me formulate my question to incorporate the effects of diet supplementation on RNA epigenetic changes.

 

Jia, G., Fu, Y., & He, C. (2013). Reversible RNA adenosine methylation in biological regulation. Trends in Genetics, 29(2), 108-115.

This paper mainly discusses the m6A RNA modification mechanism associated with regulating cell fate decisions. It helped me understand RNA epigenetics and the furthered my understanding of the mechanism associated with m6A. This proved to be helpful when figuring out how the FTO demethylase altered mRNA methylation levels.

 

McGuinness, D. H., & McGuinness, D. (2014). m 6 a RNA Methylation: The Implications for Health and Disease. Journal of Cancer Science and Clinical Oncology, 1(1), 1.

This paper discussed how m6A modification is a dynamic process and how such modifications can translate into cellular activity. Specifically it suggested how m6A impacted brain systems and was useful for me when I was in the process of relating RNA epigenetics to cellular processes and overall brain functions related to behavior. This helped me tie together key concepts regarding m6A and changes to neuronal pathways in the brain, including DA signaling.

 

Merkestein M, McTaggart JS, Lee S, Kramer HB, McMurray F, Lafond M, et al. (2014) Changes in Gene Expression Associated with FTO Overexpression in Mice. PLoS ONE 9(5): e97162.

Mice expressing two additional copies of the FTO gene (FTO-4) exhibit increased adiposity and are hyperphagic. FTO is a demethylase and targets m6A modification in RNA, which plays a role in regulating gene expression. This study examines the changes in gene expression that occur in FTO-4 mice and suggest that they up-regulate anabolic pathways and down-regulate catabolic pathways. However, no effect of FTO overexpression on m6A methylation of total mRNA was found. This paper mainly provided inspiration for the idea of upregulating FTO expression by expressing additional alleles of the gene. However, it also showed that different genes were epigenetically modified in different tissue types, suggesting FTO regulates a network of obesity related genes.

 

Pogribny IP, Karpf AR, James SR, Melnyk S, Han T, et al. (2008) Epigenetic alterations in the brains of Fisher 344 rats induced by long-term administration of folate/methyl-deficient diet. Brain Res 1237: 25–34.

This paper explained how long term administration of a folate/methyl-deficient diet led to epigenetic changes in the rat brain. This study provided insight on how the availability of methyl donors controls the activity of methyltransferases and demethylases, which inspired me to come up with my specific question.

 

Wardle, J., Llewellyn, C., Sanderson, S., & Plomin, R. (2009). The FTO gene and measured food intake in children. International journal of obesity, 33(1), 42-45.

The paper discusses how polymorphisms in the FTO gene have been linked to sensitivity to satiety in children and eating behavior. This study assisted my early research in discovering the effects the FTO gene had on feeding behavior and obesity risk.

 

Zhao, X., Yang, Y., Sun, B. F., Zhao, Y. L., & Yang, Y. G. (2014). FTO and obesity: mechanisms of association. Current diabetes reports, 14(5), 1-9.

This paper examined how variants of the FTO gene were associated with different disorders including obesity and cancer. It also introduced m6A and FTO’s role in regulating RNA processing. It ultimately summarized the functions and mechanisms of FTO through various studies and highlighted the features linked to obesity. This paper served as the basis for much of my further research regarding m6A and the role that FTO had on RNA epigenetic modifications. It also served as a good summary to tie together the key characteristics of FTO’s functions and mechanisms, which also helped me better understand its role in influencing obesity risk.

Final Project

Final Project Link:   BIOL 463 Final Project- Susan Xu

 

Reflection: 

When starting the final project, all I knew was that I wanted it to be somewhat similar to the question I proposed for the “If I were a Developmental Biologist” assignment. However, narrowing down the question to something specifically testable with one experiment was actually quite difficult and so I relied mainly on my research to direct me to a specific question. Researching was probably the hardest part of the project and reading from one paper to the next forced me to tie together any relevant information and also mentally store important facts for future reference. I then incorporated all my research and used relevant information and insights to formulate my final question.. this of course then led to even more research to assist my specific question. From this project, I learned how to come up with a hypothesis and prediction for my research question and from other papers and studies conducted. This was something I’ve never done before so all these steps that we had to take in designing a research question was new to me. When designing the actual experiment, I learned to select the technique that would specifically measure what I wanted to compare in my results. I also looked at other studies that measured similar things and so mainly got inspiration from those relevant studies. Overall, the project definitely had its ups and downs but I eventually managed to navigate through that and deal with it positively to finish the project! 🙂

Final Project Draft

Introduction

 Obesity is becoming more widespread with global projections of more than 1.12 billion obese individuals by 2030 (Kelly, Yang, Chen, Reynolds, & He, 2008). Excess fat accumulation in obese individuals occurs when energy intake exceeds energy expenditure, where their response to such imbalance is partially governed by genetic predisposition (Herrera, Keildson, & Lindgren, 2011). Twin studies have estimated heritability to account for 40-75% of the phenotypic variance of obesity in children and adults, demonstrating how the occurrence of obesity depends on the interplay of both environmental and genetic factors (Rhee, Phelan, & McCaffery, 2012). In attempts to track down common genetic variants influencing obesity, the Fat mass and obesity associated (FTO) gene was identified by genome-wide association studies (Herrera et al., 2011). Not only were genetic variants of the FTO gene associated with human adiposity and metabolic disorders, they were also linked to cancer (Zhao, Yang, Sun, Zhao, & Yang, 2014). However, the exact molecular mechanism of the effects of the FTO gene on obesity still remains largely unknown (Zhao et al., 2014).

 

Background

FTO expression is highest in areas of the hypothalamus associated with feeding, and have been shown to be linked with sensitivity to satiety in children (Wardle, Llewllyn, Sanderson, & Plomin, 2008). This suggests that the FTO gene may be influencing regulatory drivers underlying food intake (Wardle et al., 2008). The existence of single nucleotide polymorphisms (SNPs) within the gene may be responsible for an increased risk of obesity in humans since carriers of the FTO rs9939609 risk allele altered food intake, with 505 kJ and 1,231 kJ more in A allele and AA allele carriers than TT homozygotes, respectively (Zhao et al., 2014). Evidence has shown that primary transcripts containing an at-risk A risk allele at SNP rn9939609 are more abundant in blood and fibroblast RNA samples of individuals than those with the T allele (Church et al., 2011). This suggests that increased expression of FTO is correlated with obesity, which was tested in mouse models with additional copies of the Fto gene, resulting in increased fat mass and obesity via hyperphagia (Chuch et al., 2011).

 

The FTO protein is a Fe(II) and 2-oxoglutarate-dependent demethylase of single stranded DNA and RNA, which mainly targets 6-methyladenosine (m6A), 3-methyluracil (m3U) and 3-methylthymidine (m3T) (Merkestein et al., 2014). However, m3T is rare in mammalian genomic DNA, and m3U are deeply buried within folded rRNA, they are unlikely to be the physiological substrates of FTO (Jia et al., 2013). On the other hand, m6A is the most prevalent modification in eukaryotic mRNA and can affect RNA processing, RNA transport, and translation efficiency (Merkestein et al., 2014). Previous studies have shown that m6A levels in the brain are low during embryogenesis but drastically increase by adulthood, indicating that m6A plays a role in neuronal maturation and normal brain functions (McGuinness & McGuinness, 2014). Hess et al. examined the FTO protein’s control over m6A methylation and its critical role in regulating gene transcription and expression of key components in dopamine (DA) signaling in the midbrain (2013). Since FTO only targets a unique subset of mRNAs involved in neuronal function, they measured methylation on Kcnj6, Grin1 and Drd3, of which are all key regulators of DA activity (Hess et al., 2013). In the absence of FTO, mRNAs showed increased methylation and increased expression, whereas protein expression of the gene products was significantly attenuated. However, mRNA and protein expression levels of other hypermethylated mRNAs remained unchanged when FTO was absent, indicating that the effect of m6A on mRNA and protein expression is governed by specific rules or through indirect complex mechanisms (Hess et al., 2013). The studied concluded that FTO influences the translation of specific proteins in the D2R-D3R-GIRK signaling cascade, where the absence of FTO resulted in reduced protein expression which ultimately attenuated D2R and D3R signaling (Hess et al., 2013). Since dopaminergic (DA) signaling governs the control of many complex behaviors including learning, reward behavior, motor functions and feeding, FTO’s enzymatic role in regulating the neuronal pathway of the brain is of specific interest as it could provide insight on FTO’s mechanism in controlling obesity- related feeding behavior.

Increasing amounts of evidence suggest that epigenetic changes that occur on genomic DNA and histone proteins, regulating gene activity and expression patterns during development and beyond, are sensitive to extrinsic factors, such as diet and nutrients (Almén et al., 2012). Studies have shown that long-term administration of a diet lacking in methyl donors, such as folic acid, methionine and choline, caused global DNA hypermethylation in the brain (Pogribny et al., 2008). B-vitamin folate, methionine, betaine and choline are all essential for transfer reactions, which regulates the transfer of methyl groups of methylation reactions (Ishii et al., 2014). Thus, diet-induced epigenetic rearrangement during brain maturation could alter future development and behavior and even influence the onset of various diseases including obesity. Since m6A methylation states on mRNA are dynamically regulated by FTO and methyltransferase activities in response to internal and external cellular cues, is methyl donor supplementation in the diet during a developmental period sufficient to alter m6A methylation levels on mRNA and protein expression of Kcnj6, Grin1 and Drd3 in the brain? Also, does the altered diet induce similar effects in individuals overexpressing FTO?

 

Hypothesis and Prediction

Since RNA methylation involves the transfer of a methyl group similar to DNA methylation, methyl-donor supplementation in the diet during development will likely alter RNA methylation states as well. Thus, supplementation with folate, methionine, betaine and choline will be sufficient in inducing changes in m6A methylation levels on the mRNA transcripts of Kcnj6, Grin1 and Drd3. Since Hess et al. found that FTO-deficient mice displayed hypermethylation of mRNAS of Kcnj6, Grin1 and Drd3 in the brain, FTO overexpression will likely cause hypomethylation (2013). However, FTO-overexpressing mice supplemented with methyl donors should show lower levels of hypomethylation compared to mice provided a diet without supplementation. Increased levels of available methyl groups could drive greater activity of methyltransferases for increased methylation, which would thus counteract the demethylation activity by FTO.

 

Experimental Design

 Mouse Model

 The FTO-overexpression will be induced in mice by globally expressing either one (FTO-3) or two (FTO-4) additional copies of the Fto gene, as done in a study by Church et al. (2010). Wild-type C57BL/6J littermates (FTO-2) will be used as the control, expressing only 2 copies of the Fto gene. An increase in Fto mRNA expression in the brain can be confirmed later by qRT-PCR. The FTO-2, FTO-3 and FTO-4 mice populations will be kept in separate cages in a temperature and humidity controlled room on 12∶12 light-dark cycle with free access to water and food. From each of the 3 genetically different groups, half (n=5) will be fed chow highly supplemented with methyl donors (MS) while the other half supplemented with the mice chow. The MS chow will contain a 2-fold increase in folic acid, vitamin B12, choline and betaine levels relative to the control chow (Wolff, Kodell, Moore, & Cooney, 1998). Mice will be given their assigned diet starting from birth until 5 weeks of age. Previous studies have shown that FTO-4 mice begin increasing in body weight starting at 5 weeks, so mice will be killed by cervical dislocation at this point during development (Merkestein et al., 2014). This control for any methylation changes occurring as a secondary consequence of increased body weight or of other varying external factors (Merkestein et al., 2014). The brain will then be immediately dissected and kept on dry ice (-80°C) until RNA extraction.

 

MeRIP- Seq

Full-length RNA fragments in the brain will be digested to approximately 100nt long fragments following the recommendations of the sequencing platform (Illumina) (Meter et al., 2012). Immunoprecipitation of total mouse brain methylated RNA will be performed using a commercial rabbit antibody to m6A (Meyer et al., 2012). MeRIP-Seq high-throughput sequencing will be performed on replicates of midbrain RNA isolated from FTO-4, FTO-3 and FTO-2 (WT) mice. Genomic alignment will be done using the Burrows-Wheeler Aligner (BWA) and only peaks that reached significance in all replicates for each sample will be used for final peak analysis (Hess et al., 2013).

 

Gene Ontology (GO) Analysis

Peaks will be identified for all samples and the genome coordinates for FTO-4 peaks and FTO-3 peaks will be intersected with FTO-2 peaks to compare and identify any differences in m6A methylation. Specifically, UCSC Genome Browser plots of MeRIP-Seq reads for the Kcnj6, Grin1 and Drd3 genes will be analyzed, since they had been previously identified by GO analysis to regulate the DA signaling pathway (Hess et al., 2013). mRNA levels will also be determined for the three genes by quantitative PCR of all mice samples to compare their relative levels using box plots as done by Hess et al. (2013). GIRK2, GRIN1 and DRD3 protein expression levels in the midbrain tissues will also be compared across the FTO-4, FTO-3, and FTO-2 mice using SDS-PAGE and Western blot analysis, utilizing β-actin and calnexin as loading controls (Hess et al., 2013).

 

Discussion and Results

If my hypothesis is correct, mice given the MS diet will show greater levels of m6A hypermethylation of Kcnj6, Grin1 and Drd3 mRNAs relative to the un-supplemented groups. However, such hypermethylation will be to a lesser extent in FTO-overexpressing mice (FTO-4 and FTO-3) compared to FTO control mice (FTO-2) due to FTO demethylation activity. Thus, FTO-4 and FTO-3 mice will also exhibit greater GIRK2, GRIN1 and DRD3 protein expression than FTO-2 from the lesser degree of hypermethylation in both MS and control diet groups. These results would suggest that FTO functions to demethylate the mRNA of genes involved in neuronal DA pathways while increasing protein expression to enhance DA signaling activity. This could explain individuals with the risk allele and mice overexpressing FTO have the tendency to increase feeding behavior resultant from increased DA- associated activity in reward centres of the brain. If methyl donor supplementation increases methylation of DA-related genes, such a result can be useful in the development of nutrient supplementation therapies for decreasing the risk of obesity. However, if methyl supplementation is not sufficient to induce hypermethylation of Kcnj6, Grin1 and Drd3 mRNA, it will not have an affect on protein expression and thus DA reward pathways.

 

 

References

 Almén, M. S., Jacobsson, J. A., Moschonis, G., Benedict, C., Chrousos, G. P., Fredriksson, R., & Schiöth, H. B. (2012). Genome wide analysis reveals association of a FTO gene variant with epigenetic changes. Genomics, 99(3), 132-137.

 Church, C., Moir, L., McMurray, F., Girard, C., Banks, G. T., Teboul, L., … Cox, R. D. (2010). Overexpression of Fto leads to increased food intake and results in obesity. Nature Genetics, 42(12), 1086–1092.

Herrera, B. M., Keildson, S., & Lindgren, C. M. (2011). Genetics and epigenetics of obesity. Maturitas, 69(1), 41–49. http://doi.org/10.1016/j.maturitas.2011.02.018

Hess, M. E., Hess, S., Meyer, K. D., Verhagen, L. A., Koch, L., Brönneke, H. S., … & Belgardt, B. F. (2013). The fat mass and obesity associated gene (Fto) regulates activity of the dopaminergic midbrain circuitry. Nature neuroscience, 16(8), 1042-1048.

Ishii D, Matsuzawa D, Matsuda S, Tomizawa H, Sutoh C, Shimizu E (2014) Methyl Donor-Deficient Diet during Development Can Affect Fear and Anxiety in Adulthood in C57BL/6J Mice. PLoS ONE 9(8): e105750.

Jia, G., Fu, Y., & He, C. (2013). Reversible RNA adenosine methylation in biological regulation. Trends in Genetics, 29(2), 108-115.

Kelly, T., Yang, W., Chen, C. S., Reynolds, K., & He, J. (2008). Global burden of obesity in 2005 and projections to 2030. International journal of obesity, 32(9), 1431-1437.

McGuinness, D. H., & McGuinness, D. (2014). m 6 a RNA Methylation: The Implications for Health and Disease. Journal of Cancer Science and Clinical Oncology, 1(1), 1.

Merkestein M, McTaggart JS, Lee S, Kramer HB, McMurray F, Lafond M, et al. (2014) Changes in Gene Expression Associated with FTO Overexpression in Mice. PLoS ONE 9(5): e97162.

Meyer, K. D., Saletore, Y., Zumbo, P., Elemento, O., Mason, C. E., & Jaffrey, S. R. (2012). Comprehensive analysis of mRNA methylation reveals enrichment in 3′ UTRs and near stop codons. Cell, 149(7), 1635-1646.

Pogribny IP, Karpf AR, James SR, Melnyk S, Han T, et al. (2008) Epigenetic alterations in the brains of Fisher 344 rats induced by long-term administration of folate/methyl-deficient diet. Brain Res 1237: 25–34.

Rhee, K. E., Phelan, S., & McCaffery, J. (2012). Early determinants of obesity: genetic, epigenetic, and in utero influences. International journal of pediatrics, 2012.

Wardle, J., Llewellyn, C., Sanderson, S., & Plomin, R. (2009). The FTO gene and measured food intake in children. International journal of obesity, 33(1), 42-45.

Wolff, G. L., Kodell, R. L., Moore, S. R., & Cooney, C. A. (1998). Maternal epigenetics and methyl supplements affect agouti gene expression in Avy/a mice. The FASEB Journal, 12(11), 949-957.

Zhao, X., Yang, Y., Sun, B. F., Zhao, Y. L., & Yang, Y. G. (2014). FTO and obesity: mechanisms of association. Current diabetes reports, 14(5), 1-9.

In-Class Assignment #2

Group members’ names: Susan, Alanna, Rachel, Jane, Sam

Assigned paper:

Brison, N., Tylzanowski, P., Debeer, P. (2012) What the HOX is going on?

Questions:

  1. Look at the diagram and table in Figure 2. Then, look at the variety of phenotypes associated with different mutations in HOXD13. Do you notice any patterns? Would you consider the wide spectrum of phenotypes to be an advantage or a disadvantage of using human mutant phenotypes to investigate the functions and mechanisms of action of HOXD13?
  • seems that there are mainly missense mutations in Exon 2
  • expansion/contraction in polyalanine region in Exon 1à webbing between 3-4th finger (classical)
    • # of repeats correlates w/ severity of phenotype
  • Frameshift/ nonsense mutations in homeodomain (Exon 2)
  • Exon 1 mutations are dominant negative, homeodomain mutation= functional haploinsufficient

Disadvantage: more difficult to find a consistent phenotype and identify the actual gene’s function à hard to control for

– different combinations of phenotypes could be confusing

Advantage: wide range of phenotypes gives you a wider range of potential gene functions/ what it could control for (more possibilities)

 

  1. Notice how there are only 3 reported mutations in Exon 1 outside the polyAla region, but 6 in the homeobox, even though the homeobox is much shorter than Exon 1. Propose two distinct hypotheses that would explain why this might be.
  • people studying homeobox much more (more frequently) so may just happen to identify more
  • phenotypes of mutations in Exon 1 may not attract attention (even though present)
  • Exon 1 mutations may be lethal so no patient with mutation to report

 

  1. In humans, Hoxd13 looks very much like it is haploinsufficient, and the mutations reported in the paper are typically dominant (or semi-dominant/incompletely dominant/co-dominant, depending on how we look at them) to wild-type Hoxd13. Before you attempt this question, please ensure that everyone in your group knows about the two ‘ways’ in which mutant alleles can be dominant to their wild-type counter-parts (i.e. dominant negatives and dominant due to simple haploinsufficiency) and how this relates to GOF and LOF.

a) At the molecular level, how do you think the Hoxd13-expanded polyAla tract mutant exerts its ‘super-dominant negative’?

  • deformed cytoplasmic aggregates that prevents WT Hoxd13 from entering the nucleus in heterozygote
    • Negative since loses function of what Hoxd13 usually does
  • “Super dominant” à also affects Hoxd11 and Hoxd12
    • polyalanine region acts as a binding domain for the cofactors of Hoxd11 and Hoxd12 à loss of sequence similarity/ structure similarity
      • Prevents Hoxd11 and Hoxd12 from doing what they usually do

b) The reported mutations in the homeodomain (~ the homeobox) of Hoxd13 typically result in LOFs and in specific phenotypes depending on the particular mutation in question. What does this suggest? Make sure to connect the mechanistic information in the paper with your view of autopod development.

  • impairs the ability of Hoxd13 from recognizing consensus binding sequences
    • loses biding affinity
  • critical for homeodomain to maintain its amino acid sequence for specific binding to DNA consensus sequences (Eg. Stability, affinity)
  • if affect some very conserved regions in homeobox.. can prevent it from interacting w/ binding and TFs
    • depending on which amino acid you change.. could affect binding to different domains
  • relative stability/ affinity of binding to Hoxd13 protein to target could create different levels of expression of it’s target, resulting in different phenotypes (dose dependent)
  • different mutations result in different phenotypes à upstream of many regulatory pathways controlling autopod development

 

  1. A great deal of what we know about the function(s) and role(s) of HOXD13, but also of several other HOX genes, is thanks to the study of families with limb (or other) malformations much through a ‘look’ (including, ‘look for correlations’) approach.

a) In addition, and complementing this source of information, we have model systems such as the mouse, where we can selectively mutate our genes of interest in any way we want, and the chicken, which can be locally infected with vectors carrying any gene of interest. We also have the power of bioinformatics.

What are the advantages and disadvantages of each system?

  • Mouse: a lot more similar to humans (vs chicken)
  • Chicken: less labor intensive than the mouse and faster!
    • Mutations in mouse and chicken that were the same in humans result in different phenotypes compared to humans (Hoxd13 function could be diff. from species to species based on the genes its involved in regulating)
  • Human Studies: can only do studies on the specific mutations that exist
    • Results in phenotypes seen can be applied to the general population
  • Bioinformatics: can look at conserved sequences to predict phenotypes

but have to predict what the phenotype will be

b) In order for the human data to be used by researchers, the families involved have to provide informed consent. Why do you think families provide/do not provide consent? If they provide consent, what is the benefit for them? What is the benefit/value for the researchers?

  • They provide consent because…
    • hopefully find treatment down the road since their children could be affected by the same disease
    • gain insight and provide opportunities for additional research and potential future treatments
  • They don’t provide consent because…
    • Just don’t want to be part of a test –> want to keep their personal information private (cause they could be cloned..)
    • They’re just generally afraid.. scientists might use for other purposes without consent?

 

  1. What did you find most surprising in this review article?

– the array of phenotypes with mutations in a single gene!

 

Reflection:

 I remember having some difficulties with this assignment as this paper was more complex than the first. But I felt like we were able to work out any questions or confusions we may have had as a group since the questions guided our thinking and we were able to build upon our own original ideas and thoughts. The part at the end regarding consent when conducting human research was different and we came up with  some interesting points as group.

In-class Assignment #4

Assigned paper:

Chiesa et al. (2012) The KCNQ1OT1 imprinting control region and non-coding RNA: new properties derived from the study of Beckwith–Wiedemann syndrome and Silver–Russell syndrome cases

 

Questions:

  1. The authors report using OMIM to obtain some information for their research. Take a few minutes to look up Kcnq1ot1 on OMIM (http://www.omim.org) and see what information you get.
  • associated with Beckwith- Wiedemann syndrome (BWS) and a variety of human cancers
  • imprinted antisense transcript encoded by a 60-kb region
  • expressed preferentially from the paternal allele
  • produced in moth human tissues
  • CpG island within intron 10 specifically methylated on the silent paternal allele
  • When inherited maternally, deletion of LIT1 gene caused BWS with silencing p57(KIP2)
  1. Look at the pedigree in Figure 1.

a) What are a few things that can immediately be concluded about BWS (even without knowing who inherits the mutant allele from whom)?

  • Autosomal
  • Affects both males and females
  • Not lethal.. but there are also people who die

b) II-2 and II-4 both have BWS, and both have one child with BWS and one child without BWS. Briefly explain how this is possible.

  • BWS is only on one allele.. since the child receives only one allele from each parent … the child only has 50% of inheritance of BWS

 

  1. Both the BWS and the SRS patients have duplications of parts of the locus being studied, and so does Individual I-4, who has no syndrome. Using the information in Figure 5 and Figure 8, propose a hypothesis that explains the differences in phenotype (both macroscopic phenotype and the DNA methylation pattern phenotype) among the patients with BWS, SRS, and Individual I-4.
  • figure 5 shows that I-4 duplication has minimal methylation whereas the SRS patient has more methylation of one of the duplicated alleles

–> duplicated on the paternal allele

  • methylation on one of the duplicated alleles could contribute to the disease phenotype (macroscopic)
  • Figure 8 shows that BWS and SRS patients both have duplications on the maternal allele whereas I-4 has duplication on the paternal allele
    • BWS: duplication of paternal allele on the maternal allele
    • SRS: duplication of the maternal allele on the maternal allele
    • I-4: duplication of the paternal allele on the paternal allele

–> any duplication occurring on maternal allele will cause a disease phenotype

(regardless of whether it is a maternal or paternal duplication)

  1. Explain what the data in Figure 7 show, and how you interpret them in terms of the role of Kcnq1ot1 in the regulation of the imprinted cluster being studied.
  • Kcnq1ot1 is involved in folding enrichment in BWS patients in the maternal allele
  • Shows that Kcnq1ot1 RNA binds to H3
  • B—significant difference in the amount binding between the BWS patients and the control (increased binding of BWS patients on the maternal allele)
    • Normally no expression on the maternal chromosome… so maybe production from the maternal allele is causing the disease phenotype

– not as much of a difference seen on the paternal allele… also see no effect phenotypically when inherit allele paternally

 

  1. Optional/Time permitting: Take a look at the phenotypes of the SRS and BWS patients. Do you notice any trends? Knowing that all the patients studied in this article have mutations in the same imprinted cluster, what could explain the differences in phenotypes? Knowing the effects at the molecular (DNA methylation/gene expression) of the various mutations, how could these macroscopic phenotypes be explained?

 

Reflection: I chose to include this assignment since we struggled to make sense of the pedigree at first but overcame that as we worked through the assignment as a group. It was also interesting to read a paper on a specific disease as I feel like I am always more interested in reading things when they pertain to disease phenotypes.. Not sure why. But overall, I thought we worked well as a group to overcome any confusions we may have had in the beginning and ended up clarifying and questions we had while we worked though the assignment.

Project Outline

Student’s name: Susan Xu

Topic chosen: RNA epigenetics associated with obesity risk

SPECIFIC QUESTION: Is a diet supplemented with methyl donors sufficient to alter RNA methylation changes to attenuate the risk of obesity?

HYPOTHESIS: A methyl donor supplemented diet will increase methylation of mRNA of specific genes associated with the DA pathway involved in feeding and reward behaviour. Increasing methylation at these sites will decrease protein expression and result in reduced feeding behaviour. This will attenuate any effects FTO overexpression has on such loci that increases feeding behaviour and the risk of developing obesity.

 

EVIDENCE ON WHICH THE HYPOTHESIS IS BASED (INCLUDE REFERENCES):

Wardle, J., Llewellyn, C., Sanderson, S., & Plomin, R. (2009). The FTO gene and measured food intake in children. International journal of obesity, 33(1), 42-45.

  • FTO expression in the brain is greatest in the hypothalamus associated with feeding
  • FTO linked to snensitivity to satiety in childrenà so influencing a regulatory driver underlying food intake?
  • Children with two copies of lower-risk alleles ate less than two higher-risk alleles
  • T allele is protective against overeating by internal signals of satiety

Almén, M. S., Jacobsson, J. A., Moschonis, G., Benedict, C., Chrousos, G. P., Fredriksson, R., & Schiöth, H. B. (2012). Genome wide analysis reveals association of a FTO gene variant with epigenetic changes. Genomics, 99(3), 132-137.

  • DNA methylation is sensitive to extrinsic factors such as diets and nutrients
  • A central epigenetic mechanism is methylation of DNA cystosine residues, which may decrease transcription of genes
  • FTO is a demethylation enzyme and may influence the methylation level of other genes
  • It is structurally similar to AlkB family of enzymes that remove methyl groups from DNA residues

Hess, M. E., Hess, S., Meyer, K. D., Verhagen, L. A., Koch, L., Brönneke, H. S., … & Belgardt, B. F. (2013). The fat mass and obesity associated gene (Fto) regulates activity of the dopaminergic midbrain circuitry. Nature neuroscience, 16(8), 1042-1048.

  • inactivation of FTO gene impairs DA pathway functions and behavioral responses
  • increased m6A methylation on subset of mRNAs important for neuronal signaling, including DA pathway
  • FTO regulates the demethylation of specific mRNAs in vivo which relates to the control of DA transmission

 

PREDICTION(S):

Control mice + Normal diet à WT mRNA methylation, Normal feeding behaviour

FTO overexpressing mice + Normal diet à Decreased mRNA methylation, Increased feeding

Control mice + Methyl donor diet à Increased mRNA methylation, Decreased feeding

FTO overexpressing mice + Methyl donor diet à Slight decrease of mRNA methylation, Slight increased feeding

 

EXPERIMENTAL APPROACH TO TEST PREDICTION (INCLUDE ANY DETAILS THAT YOU HAVE WORKED OUT SO FAR):

  • expose mice to methyl-donor diet or control diet for both FTO-overexpressing and WT groups
  • obtain brain tissue after 5 weeks of development

MeRIP- Seq:

  • fragment RNA to 100nt long and immunoprecipitate m6A methylated RNA by using a rabbit antibody to m6A
  • perform high throughput sequencing and use Burrows- Wheeler Aligner (BWA) to align the genome and select for peaks that reach significance

GO Analysis:

  • intersect peaks from FTO-overexpressing group and FTO-normal group to compare similarities and differences of m6A methylation
  • analyse peaks for specific genes involved in DA signalling pathway
  • use quantitative PCR to measure mRNA levels of samples
  • use Western blot analysis to determine protein expression levels of selected DA pathway genes

LIST OF RELEVANT PRIMARY AND REVIEW ARTICLES READ, AND SUMMARY OF RELEVANT INFORMATION FROM EACH (this is the start of an annotated bibliography):

http://www.sciencedirect.com/science/article/pii/S1046202314002308

  • an overview of MeRIP-Seq protocol

http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0097162#s2

Merkestein M, McTaggart JS, Lee S, Kramer HB, McMurray F, Lafond M, et al. (2014) Changes in Gene Expression Associated with FTO Overexpression in Mice. PLoS ONE 9(5): e97162.

  • Mice expressing two additional copies of the FTO gene (FTO-4) exhibit increased adiposity and are hyperphagic. FTO is a demethylase and targets m6A modification in RNA, which plays a role in regulating gene expression. This study examines the changes in gene expression that occur in FTO-4 mice and suggest that they up-regulate anabolic pathways and down-regulate catabolic pathways. However, no effect of FTO overexpression on m6A methylation of total mRNA was found.

http://journals.plos.org/plosone/article?id=10.1371/journal.pone.0105750

Ishii D, Matsuzawa D, Matsuda S, Tomizawa H, Sutoh C, Shimizu E (2014) Methyl Donor-Deficient Diet during Development Can Affect Fear and Anxiety in Adulthood in C57BL/6J Mice. PLoS ONE 9(8): e105750.

Methyl donors, such as folic acid, methionine, and choline are related to one-carbon metabolism and mediate methylation. This study examines the effects of methyl donor deficiency during a developmental period in fear memory acquisition/extinction and anxiety-like behavior. Results showed that methyl donor deficiency caused mice to have an impaired fear memory acquisition and reduced anxiety-like behavior by decreasing the expression of Dnmt3a, Dnmt3b, Grin2b and Gabar2.

 

HOW DOES THE QUESTION FIT INTO THE BROADER PICTURE, AND WHAT IS ITS IMPACT?

  • certain genes have been identified for increasing the risk for obesity while other factors such as excess gestational weight, diabetes, and smoking can also influence the risk
  • understanding the factors influencing obesity risk can help target certain behaviours and exposures to decrease the prevalence of obesity
  • we can gain more insight on how the FTO can alter gene expression to increase the risk of obesity
  • since supplementing human diets with methyl donors would be difficult to conduct and control, animal studies can provide insight to such epigenetic mechanisms that result

POTENTIAL WAYS TO MAKE YOUR QUESTION KNOWN TO THE PUBLIC AT LARGE (OR TO YOUR NON-BIOLOGIST FAMILY AND FRIENDS):

  • understanding the mechanisms governing obesity risk can help parents and children change certain behaviours and exposure during critical times during development that may modify one’s genetic predisposition

Techniques Project: qPCR

  1. Names and contributions of group members:

Alanna: Research, Write-up, Powerpoint

Susan: Research, Write-up, Powerpoint

Rachel: Research, Write-up, Powerpoint

Jane: Research, Write-up, Powerpoint

Sam: Research, Write-up, Powerpoint

  1. Technique chosen:

RT-PCR: Real time PCR or Quantitative PCR (qPCR)

  1. What does this technique ‘do’?

Amplification and detection of DNA simultaneously in Real Time.

  1. What applications is this technique employed for?
  • Gene expression analysis or mRNA analysis
    • Hein et al. (2001) employed real time PCR to analyze murine gamma interferon-gamma mRNA (a cytokine mRNA) expression in splenocytes
  • Detection of GMOs in food
    • Zeitler et al. (2002) identified real time PCR as a method for quantifying transgenic contaminants with herbicide resistance in conventional rape seed.
  • Cancer or disease detection
    • Multiplex real-time reverse transcriptase PCR is an applicable method for the detection, identification, and quantification HBV, HCV and HIV-1
    • Bernard and Wittwer (2002) used real-time PCR for detection of multiple breast cancer molecular markers
  • Genetic variation analysis
    • Real-time PCR is able to detect mutations in the sequence, including single nucleotide polymorphisms (SNPs) through its melting point analysis.

5.  What questions relating to gene regulation and/or development can be addressed using this technique? Provide two examples (peer-reviewed papers) that use this technique.

Cytokine gene expression and regulation during infection:

Example: Th1 and Th2 cytokine gene expression in primary infection and vaccination against Fasciola gigantica in buffaloes by real-time PCR.

Cytochrome expression and regulation in different life stages (unfertilized eggs, embryos/larvae and adult tissue) and its role on neurodevelopment and plasticity:

Example: Real-time PCR analysis of cytochrome P450 aromatase expression in zebrafish: Gene specific tissue distribution, sex differences, developmental programming, and estrogen regulation.

  1. What critical reagents are required to use this technique?
  • Taqman based real-time PCR
    • Primers, Taq polymerase, Mg2+, Nuclease free H2O, dNTPs, Reverse transcriptase (if starting material is RNA), Taqman probes, appropriate buffers and DNA template.
  • SYBR Green based real-time PCR
    • Primers, thermophilic DNA polymerase, Mg2+, SYBR green I dye, Nuclease free H2O, dNTPs, Reverse transcriptase (if starting material is RNA), appropriate buffers and DNA template.
  • Other materials include: Real-time PCR machine that is able to complete thermal cycling steps for PCR and collect fluorescence data simultaneously, a computer, and suitable computer software for data collection and analysis.
  1. What critical information is required to be able to employ this technique?
  • Sequence data on the target sequence to design proper probes and primers.
  • Melting temperatures for PCR products for melting curve analysis to determine amplification specificity.
  1. References:

Bernard PS, Wittwer CT. Real-time PCR technology for cancer diagnostics. Clin Chem 2002; 48:1178–1185.

Bustin SA, Mueller R. Real-time reverse transcription PCR (qRT-PCR) and its potential use in clinical diagnosis. Clinical Science 2005; 109:365-379.

Hein J, Schellenberg U, Bein G, Hackstein H. Quantification of murine IFN-γ mRNA and protein expression: impact of real-time kinetic RT-PCR using SYBR Green I dye. Scand J Immunol 2001; 54:285–291

Kumar N, Raina OK, Nagar G, Prakash V, Jacob SS. Th1 and Th2 cytokine gene expression in primary infection and vaccination against Fasciola gigantica in buffaloes by real-time PCR. Parasitol Res 2013; 112:3561-3568.

Sawyer SJ, Gerstner KA, Callard GV. Real-time PCR analysis of cytochrome P450 aromatase expression in zebrafish: Gene specific tissue distribution, sex differences, developmental programming, and estrogen regulation. General and comparative Endocrinology 2006; 147:108-117.

Valasek MA, Repa, JJ. The power of real-time PCR. Adv Physiol 2005; 29: 151-159.

Zeitler R, Pietsch K, Waiblinger H. Validation of real-time PCR methods for the quantification of transgenic contaminations in rape seed. Eur Food Res Technol 2002; 214:346-351.

 

Our revised question: 

Which of the following statements are TRUE?

A) One advantage of real time PCR is that it can be performed at a single temperature without the need for specialized equipment.

B) If a DNA polymerase other than Taq polymerase was placed in the TaqMan qPCR reaction, the target sequence will be amplified but it will not be detected by the machine.

C) In an experiment, we want to find a mutation in our gene of interest by melt curve analysis, we can use SYBR Green method of qPCR.

D) Use of gel, low sensitivity and poor precision are all draw backs of traditional PCR

E) Contamination by DNA fragments with no sequence homology to the target sequence can show up as a false positive in TaqMan method but not in SYBR Green Method.

 

Link to powerpoint presentation:  https://docs.google.com/presentation/d/150EOQskwstkJAW_c45nkrYdH_an7zSkDElTfQb3a3Dg/edit#slide=id.gbd6576bcc_0_25

 

Reflection:

I chose our techniques project as one of my top assignments as I felt like it was different from all the others since it was the first assignment that really forced us to work on something as a collective group. Starting with our research for the qRT-PCR, I learned to search and extract relevant information literature effectively and most importantly simplify all the technical details of the method so that it could be better understood. As a group we were able to identify key characteristics and traits of the technique to include in our presentation and we tried to communicate that information clearly during the actual presentation by outlining key facts and points we found to be of particular importance. This project also let me assess my own knowledge of qRT-PCR which was introduced to me in BIOL 335 and I found that I had to relearn the procedures for the technique to fill in any gaps from what I could remember. Overall, this project was a great group effort and really taught us how to collaborate and work together as a group for the rest of the semester. We also established a facebook group as a way to communicate our ideas and collectively work on assignments if we couldn’t meet in person. I also really enjoyed the Techniques Café part of the project in that it allowed us to see what other groups had done and how they chose to present their projects.

A Genetic Switch to Determine Aging?

Article:

http://www.sciencedaily.com/releases/2015/07/150723125244.htm

The study of C. elegans has led to the discovery that cells begin the aging process as soon as an animal reaches sexual maturity. A genetic switch that turns off cell stress responses that protect the cell itself in stressful environments is responsible for the aging process. This genetic switch is conserved in all animals including humans and offers a target for future studies. Perhaps there could a way to turn the genetic switch back on to protect cells from aging while resisting stress. This would be widely beneficial in that it could possibly reduce the susceptibility to age-related diseases. In an experiment where germline cells were blocked from sending signals to turn off cellular quality control, somatic cells remained stress resistant and robust in adult animals. This signal can then be a useful target for future research related to disease and aging, and could possibly help us develop potentials for living longer and healthier lives. Overall, it was surprising to see that our cells start becoming less resistant to stressful stimuli right when we hit sexual maturity and that the process starts so abruptly! This comes to show that there are signals produced throughout development that signal other various cellular mechanisms, such as the one seen in pubertal onset. By manipulating these signals through environmental stimuli or factors could provide and avenue for possible research to elucidate the specific cellular mechanisms involved in regulating development. This could thus allow us to control for the onset of specific processes and perhaps even delay aging and various diseases!

The Environment Affects Epigenetics and Disease

Article:

http://www.sciencedaily.com/releases/2015/08/150803083351.htm

I’ve always had more interest in epigenetic changes and diseases influenced by environmental factors and this article reevaluates the importance of such factors. Although some genetic mutations may be inherited, others are largely caused throughout one’s life through exposure to different environmental changes that have an affect gene expression. This proves to be the reason why we may see some diseases having a later onset than others. Researchers have studied how epigenetic modifications can be passed on to subsequent offspring and between generations even when the DNA remain unchanged. They have also found various environmental toxicants such as plastics, pesticides, fungicide, dioxin and hydrocarbons that contribute to disease even three generations later. Changes of DNA structure, such as copy-number variations, have been observed in third generation offspring as well. This comes to show that environmental factors and epigenetic changes can drive genetics and be the main drivers of intergenerational changes observed. This makes me think about how my environmental exposure today could possibly alter the genes of my great great grandchildren, which is actually a bit frightening to say the least.

Cells Rhythmically Regulate Genes!

Article:

http://www.sciencedaily.com/releases/2015/10/151021135929.htm

This article introduced the idea of “pulsing” for controlling gene expression rhythmically. The idea is that cells activate and deactivate transcription factors causing protein interactions to go in and out of sync and gene expression to go up and down. This could underlie core cell processes including responses to stress. To test this, the researchers set up time-lapse movies to track two pulsing proteins (Msn2 and Mig1) and a target gene in yeast cells. When the yeast cells were stressed, Msn2 and Mig1 changed their pulse timing, with either more or less overlap between pulses, depending on the stimulus. As a result of the altered rhythms, the cells were able to produce more proteins that helped the yeast cope with stressful situations. While combinatorial regulation accounts for parts of gene regulation, this new study sheds light on the relative timing of pulsing transcription factors may be equally important in regulating cell functions and responses. This new mode of regulation may be critical in understanding the combinatorial regulation of complex genetic networks governing various cell processes. This reminds me of something I learned in BIOL 455 this semester, when we talked about protein and transcription activation governing circadian rhythms by endogenous cell oscillators. The oscillators also function through rhythmic pulses that either inhibit or activate certain proteins, which ultimately determine and regulate the sleep- wake cycle. I think future research should explore the effects of time-based regulation on cellular processes and gene regulation as it could provide important insight to how our biological systems interact with one another to regulate complex interacting networks.

A Single Gene with a Huge Role in Brain Development!

Article:

http://www.genengnews.com/gen-news-highlights/single-gene-found-to-play-huge-role-in-brain-development/81251997/

This was an interesting article that introduced a newly discovered gene, NeuroD1. NeuroD1 allows the formation of new brain cells by acting as a master regulator of a large number of genes involved reprogramming transcription factor and chromatin required for neurogenesis. The understanding of such a gene and how the brain develops in the first place is crucial for developing treatments for neurodegenerative disorders such as Parkinson’s, where neurons are irreversibly lost. In the paper, Dr.Tiwari and his colleagues showed that NeuroD1 is only expressed in brain stem cells and epigenetically turns on genes that are normally turned off during development. Surprisingly, the genes remain switched on even when NeuroD1 is later switched off, suggesting that permanent epigenetic marks are left to guide neuronal differentiation in the cell. This is similar to how iPSCs are exposed to different reprogramming factors that drive differentiation to become a specific cell type. This new discovery can thus aid future advancements in stem cell technology and therapies.

Network of Genes to Control When Puberty Begins

Article:

This was a recent article released regarding research that demonstrated how the ZNF (Zinc finger) gene family acts as a puberty “break” by repressing the network of genes that initiate pubertal development. This was interesting to me as I’ve always wondered why girls today are beginning puberty a lot earlier. The paper’s new discovery could allow scientists to assess whether environmental factors, such as nutrition or human-made products, may accelerate reproductive development by epigenetically inhibiting gene repressors (ZNFs). ZNFs are thought to act epigenetically by promoting the loss of H3K4me2, which is normally associated with gene activation, at gene regions that facilitate puberty. Thus, when levels of ZNFs decrease in the hypothalamus around late prepubertal development, the “break” is released and puberty begins. Such a discovery can promote new avenues for treating precocious puberty and its associated risks of breast, ovarian and uterine cancer.